Key words: Chagas disease. Fecaloma. Megacolon. Surgical treatment. Palabras clave: Enfermedad de Chagas. Megacolon. Fecaloma. Tratamiento quirúrgico. Diagnóstico y tratamiento de la enfermedad inflamatoria intestinal: Primer . bolsa, anastomosis íleo-anal, pouchitis, complicaciones, megacolon tóxico y. JARAMILLO BARBERI, Lina Eugenia. Proposed Recommendations and Guidelines for Diagnosis of Hirschsprung’s Disease in Mucosal and Submucosal .

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HD is a hirdchsprung anomaly that occurs due to a discontinuation of the cranial-caudal migration of neural crest cells, which are responsible for innervation of the colon, or when the ganglion cells undergo premature death between 5th and 12th weeks of pregnancy.

The patient underwent conservative treatment with good evolution and was discharged without surgical intervention. The other is the Habr-Gama technique that causes the posterior colorectal anastomosis, immediately, with acceptable results 8. Discussion HD is a congenital anomaly that occurs due to a discontinuation of the cranial-caudal migration of neural crest cells, which are responsible for innervation of the colon, or when the ganglion cells undergo premature death between 5th and 12th weeks of pregnancy.

C Surgical margin with ganglion cells. Chagas disease CHD is endemic in the Americas but due to increased immigration is becoming increasingly common siagnostico our country. A new surgical method for the treatment of chagasic megacolon. Duhamel-Haddad Procedure is also a good option. Several procedures are used to manage this disease after childhood; currently the option of choice is the surgical procedure of Duhamel. A hypothesis of HD was proposed; thus an anorectal manometry was asked, but its result was inconclusive due to patient’s lack of cooperation.

Enfermedad de Hirschsprung en el adulto. This is an open-access article distributed under the terms of the Creative Commons Attribution License. Serology for Chagas’ disease was carried out in order to exclude a diagnosis of Chagas’ Disease megacolon, with negative result. In addition, enferemdad reported symptoms caused the girl’s parents to begin to justify such a fact as a result of some psychological, rather than organic, disorder.


Hirschsprung’s Disease HDalso known as hirschsprunt aganglionic megacolon, is an anomaly characterized by an absence of ganglion cells in the myenteric and submucosal plexuses in a variable bowel segment.

The diagnosis depends on the stage of the disease and treatment is applicable only in the acute phase. Some cases involve gene mutations for endothelin-B receptor. Principles and practice of surgery for the colon, rectum and anus.

Enfermedad de Hirschsprung | Osceola Surgical Associates

Gastrointestinal manifestations of Chagas’ disease. The absence of ganglion cells results in permanent contraction of the dde segment, preventing the passage of fecal content through that region.

Niger J Clin Pract. In addition, it is established that factors related to gender play a role, since men are preferentially affected, at a frequency of 4: The enteric hirsxhsprung system in chagasic and idiopathic megacolon.

The blood test with tumor markers was normal and an abdominal CT objectived fecal and recto-sigmoid colon dilation Fig. Surgery of Chagasic megacolon. Conservative treatment is reserved for patients oligosymptomatic or with surgical contraindications 5.

Nevertheless, the literature considers as the procedure of choice the Duhamel technique in only one surgical diagnostio, 2 which reduces the hospitalization time. Subsequently, new variations have been postulated as the rectosigmoidectomy with ileal interposition, with good results and decreased recurrence 9, This surgery is considered curative.

Some patients reach adulthood without a diagnosis for this disease. Rev Argent Resid Cir. Am J Gastroenterol ; During admission the patient was interrogated again and in her family history stands out the death of his mother for cardiac disease at the age of Informe de um caso. It is caused by Trypanosoma diagnoztico 1 that is transmitted by blood-sucking insects, blood transfusions or fetal transmission 1,2.


Enfermedad de Hirschsprung

The technique considered as the golden standard for the diagnosis of HD is the absence of ganglion cells in diagnostic rectal biopsy specimen. Enterocolitis, constipation and fecal incontinence represent the main postoperative complications in children. In this latter case, HD may affect the entire colon and even the small intestine.

This disorder is uncommon in adolescence and in adulthood and when present in this age group, it shows up as an ultrashort-segment disease. Treatment of megacolon secondary to CHD should be to prevent surgical complications.

We report a case of a patient 41 years old, from Argentina, who went to the emergency room with abdominal pain and constipation. Dis Colon Rectum ;46 11 On examination, she presented lower abdominal discomfort with feeling lower abdominal mass.

However, post-operative bowel functioning is not always satisfactory. Cleansing hrschsprung are effective and fibrocolonoscopy was normal. Rectosigmoidectomy with Ileal Loop Interposition. This factor contributed to the delay in her diagnosis, driving the pediatrician out of a HD hypothesis.

Critical analysis of outcome in operative methods. Gordon PH, Nivatvongs S. Dis Colon Rectum ; Most patients with CHD have some type of heart disease, so they tend to be high risk for surgery 6.